Severe mitral regurgitation due to coronary arteritis of mucocutaneous lymph node syndrome A new surgical entity

Mucocutaneous lymph node syndrome in two siblings.

Severe mitral regurgitation due to mitral valve prolapse associated with Bland-White-Garland syndrome.

Bland-White-Garland syndrome refers to the rare congenital cardiac abnormality whereby the left coronary artery arises from the pulmonary artery. The natural history of this condition is highly variable, ranging from death in early infancy to asymptomatic adult survival. It is sometimes diagnosed in adults with mitral regurgitation thought to be of ischaemic origin. We report a case of a 29-yea...

Unstable angina in a patient with mucocutaneous lymph node syndrome.

An 11-year-old boy with mucocutaneous lymph node syndrome, who later developed an acute anteroseptal infarction and unstable angina, is presented. Anginal attacks were shown by 24-hour long-term ambulatory electrocardiographic recording. He was shown to have multiple coronary aneurysms with thrombi, and underwent a successful aorto-coronary bypass.

Mitral valve aneurysm due to severe aortic valve regurgitation.

A33-year-old man presented to the hospital with shortness of breath and chest pain. He was subsequently diagnosed with Streptococcus mitis endocarditis involving the aortic valve. The initial echocardiogram revealed moderate aortic valve regurgitation and a normal mitral valve without regurgitation. The patient was treated with afterload reduction and antibiotics. Blood cultures were negative w...

Cross-sectional echocardiographic diagnosis of coronary artery aneurysms in patients with the mucocutaneous lymph node syndrome.

Real-time cross-sectional echocardiographic studies revealed the presence of coronary artery aneurysms in five patients with mucocutaneous lymph node syndrome. These lesions appeared as circular echo-free spaces with clearly-defined borders in sites corresponding to angiographically proven aneurysms. In 15 normal subjects who were studied only by noninvasive methods, and in 17 who had normal co...